非致密性心肌病(noncompaction cardiomyopathy,NCCM)是一种遗传异质性疾病,近年来的发病率逐渐提高,但对其诊断和预后评估一直是临床上的重要挑战.心脏磁共振(cardiac magnetic resonance,CMR)成像能够提供心肌结构、功能、活性以及组织定量等多方面的信息,在心肌病领域发挥出独特优势.本篇综述围绕NCCM相关的CMR技术展开,就常规CMR技术及CMR新技术在NCCM诊断及预后评估中的应用进展予以总结,旨在深入探讨NCCM的发病机制、提高早期检出率,进而有效指导临床治疗以改善患者预后.同时,希望通过总结前人的研究工作,为新技术在该病中的研究提供参考.
Progress in diagnosis and prognosis of noncompaction cardiomyopathy with multimodal cardiac magnetic resonance
Noncompaction cardiomyopathy (NCCM) is a genetically diverse condition that has seen a rise in prevalence in recent times,yet its diagnosis and prognosis evaluation pose significant clinical hurdles. Cardiac magnetic resonance (CMR) imaging can provide comprehensive information about myocardial structure,function,viability,and tissue quantification,offering unique advantages. This review focused on NCCM-related CMR techniques,and summarized the application progress of conventional CMR techniques and new CMR techniques in the diagnosis and prognosis assessment of NCCM. The purpose of this study is to investigate the pathogenesis of NCCM and improve the early detection rate,so as to effectively guide clinical treatment and improve the prognosis of patients. At the same time,it is hoped that by summarizing the previous research work,it can provide reference for the research of new technology in the disease.
noncompaction cardiomyopathycardiac magnetic resonancemultimodal magnetic resonance imagingdiagnoseevaluation of prognosis
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