Objective To investigate the imaging manifestations of moyamoya disease in children by conventional MRI and to improve the understanding of the disease.Methods The MRI data of 24 children with moyamoya disease confirmed by DSA were retrospectively analyzed.The imaging manifestations of the cases were observed,and chi-square test was used to analyze the trend of abnormal indications in different stages.Results There were 21 bilateral cases and 3 unilateral cases,a total of 45 sides.Conventional scan revealed 38(84.4%)slender horizontal segments of the middle cerebral artery;abnormal small vessels were found in 26 sides(57.8%)of basal ganglia.T2-FLAIR showed"ivy sign"in 36 sides(80.0%)and"me-dullary streaks sign"in 38 sides(84.4%).23 sides(51.1%)of cerebral white matter showed patchy hyperintense lesions on T2WI,and 5 sides(11.1%)showed malacia foci.There were acute cortical infarction in 11 sides(24.4%)and local cortical atrophy in 10 sides(22.2%).There were significant differences in the incidence of M1 segment slender and"medullary streaks sign"in different stages(P<0.05),while there were no significant differences in the incidence of other abnormal in-dications in different stages(P>0.05).Conclusion In children with moyamoya disease,the M1 segment of the affected side is more slender,abnormal small blood vessels can be seen in the basal ganglia,T2-FLAIR of the affected side of the brain can show"ivy sign"and"medullary streaks sign",there may be localized ischemia or softening foci in the white matter,and the cortex can be accompanied by acute infarction or softening or atrophy.Conventional MRI can provide important diagnosis for the detection of moyamoya disease in children.