肺泡蛋白沉积症的诊疗进展
Progress in diagnosis and treatment of alveolar proteinosis
常晓青 1李丹丹 1胡莎莎 1范儒旭 1李英1
作者信息
- 1. 河南大学人民医院呼吸与危重症医学科,河南 郑州 450003
- 折叠
摘要
肺泡蛋白沉积症是一种罕见的肺部疾病,其表面活性物质在肺泡巨噬细胞和远端气道积聚,导致气体交换受损,从而引起呼吸困难和低氧血症.自 1958 年首次报告以来,临床对该疾病的发病机制、诊断、治疗等方面的认识有很大进展.本文主要就肺泡蛋白沉积症的发病机制、诊断、治疗进行综述.
Abstract
Alveolar proteinosis is a rare lung disease in which surfactant accumulation in alveolar macrophages and distal airways leads to impaired gas exchange,resulting in dyspnea and hypoxemia.Since the first report in 1958,the clinical understanding of the pathogenesis,diagnosis and treatment of the disease has made great progress.This article reviews the pathogenesis,diagnosis and treatment of alveolar proteinosis.
关键词
肺泡蛋白沉积症/发病机制/诊疗进展Key words
Alveolar proteinosis/Pathogenesis/Progress of diagnosis and treatment引用本文复制引用
出版年
2024
NETL
NSTL
维普
万方数据