Hereditary angioedema(HAE)is a rare autosomal dominant condition characterized by episodes of swollen of the upper airway,intestines,and skin.The primary pathogenesis is the reduction in the function and/or plasma concentration of complement 1 esterase inhibitor(C1-INH).When edema involves the gastrointestinal tract,abdominal pain will be the main manifestation,which is often difficult to differentiate from surgical acute abdomen and may lead to misdiagnose and mistreatment.This paper reported a case of HAE with recurrent abdominal pain as the main manifestation,which diagnostic course was rugged and complicated.Eventually,the diagnosis was confirmed by testing the function and concentration of C1-INH,and a satisfactory clinical outcome was achieved after prophylactic treatment with Lanndelumab.
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