摘要
钙化性纤维性肿瘤(calcifying fibrous tumor,CFT)是一种以钙化、沙砾小体等为特征性表现的良性间充质病变,其主要成分为胶原化的纤维结缔组织.CFT可以发生于任何年龄,相对好发于女性,其发病部位有胸膜、胃肠道、纵隔、心脏、肺部、颈部、背部、腹股沟、四肢等.其中发生于胃部的病例较少,以病例报道为主.目前对胃CFT的病因、临床表现、影像学特点以及治疗和预后的探索也并不深入.本例胃CFT的特殊性在于肿瘤发生在胃体大弯侧浆膜层下,并呈外生性发展,与胃壁间有蒂相连,早期可能不在胃囊内形成明显隆起,难以被常规胃镜检查检出,与目前报道较多的内生性CFT有明显区别.本病例报道能为具有类似临床表现的胃CFT患者的诊断方向及治疗方案提供一定的提示和指导.
Abstract
Calcifying fibrous tumor(CFT)is a kind of benign tumor composed mainly of large amounts of collagenized fibrous connective tissue,which may be accompanied by calcification,gravel vesicles,and other characteristic manifestations.CFT can occur at any age and is relatively more prevalent in females.CFT usually occur in the pleura,gastrointestinal tract,mediastinum,heart,lungs,neck,back,groin and limbs,but not commonly occurs in the stomach.Gastric CFT is uncommon and is mainly reported as case reports.The etiology,clinical manifestations,imaging examinations,treatment and prognosis of gastric CFTs have not been thoroughly studied.The specificity of this case is that the tumor developed under the serosal layer of the greater curvature of the gastric body,it was exophytic and connected to the gastric wall by a pedicle.In the early stage,exophytic gastric CFT may not form a distinct bulge in the gastric pouch,and is difficult to be detected by conventional gastroscopy,which is distinctly different from endophytic CFTs(main type reported so far).This case report can provide certain hints and guidance for the diagnostic direction and treatment plan of gastric CFT patients with similar clinical manifestations.
维普
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