Zinner综合征1例并文献复习
Zinner syndrome:a case report and literature review
杨延梦 1张烽 1唐艳隆 1毕孝杨1
作者信息
- 1. 大理大学第一附属医院放射科,云南 大理 671000
- 折叠
摘要
目的 探讨Zinner综合征的诊治要点,降低误诊率.方法 回顾性分析 1 例Zinner综合征患者的临床资料.以Zinner综合征、肾缺如以及精囊囊肿作为检索词,对以下数据库截至 2022 年 11 月收录的文献进行检索:PubMed、CNKI、万方数据知识服务平台、维普中文科技期刊数据库,收集并分析检索到的以血尿、尿频、尿痛等泌尿系统症状为首发表现的Zinner综合征病例,总结其临床特征、发育特点、治疗方法等.结果 该例患者为 46 岁男性,因发现膀胱占位性病变 8 年、出现血尿伴尿痛 1 周入院,经影像学检查确诊为Zinner综合征.接受经尿道膀胱镜检术+经直肠精囊囊肿抽吸术治疗,术程顺利,于术后第 2 日出院,遵医嘱于院外继续接受抗感染治疗.检索文献,共收集到 16 例以血尿、尿痛等泌尿系统症状为首发表现的Zinner综合征病例,均通过影像学检查发现泌尿系统异常,主要治疗方法是手术切除囊肿、囊肿穿刺抽吸等.接受了随访的 8 例患者中 7 例未见复发、1 例接受精囊囊肿穿刺抽吸治疗的患者疑似复发.结论 Zinner综合征主要影像学表现为单侧精囊囊肿、同侧肾缺如和同侧射精管阻塞,超声检查、CT、MRI均是诊断Zinner综合征的重要手段,实施手术切除不易复发.
Abstract
Objective To investigate the key issues of clinical diagnosis and treatment of Zinner syndrome and reduce the misdiagnosis rate.Methods Clinical data of 1 case of Zinner syndrome were retrospectively analyzed.Zinner syndrome cases presenting hematuria,frequent urination and dysuria as initial manifestations were retrieved from PubMed,CNKI,Wanfang Data and Chongqing VIP until November 2022 by using the searching words of Zinner syndrome,renal agenesis and seminal vesicle cyst.Clinical characteristics,developmental characteristics and treatment methods were summarized.Results The 46-year-old male patient was admitted to the hospital because of"bladder space-occupying lesion for more than 8 years,hematuria with dysuria for 1 week",and was diagnosed with Zinner syndrome by imaging examination.He successfully underwent"transurethral cystoscopy+transrectal pelvic mass puncture biopsy",and was discharged from the hospital at postoperative 2 d.The patient was advised to continually receive anti-infection treatment after discharge.According to literature review,16 cases of Zinner syndrome presenting with hematuria,dysuria and other urinary symptoms as the first manifestations were collected.All patients developed abnormalities in the urinary system by imaging examination.Surgical resection and puncture biopsy were the main treatment methods.Among 8 patients receiving follow-up,7 cases did not recur,and 1 suspected recurrent case underwent puncture biopsy.Conclusions Zinner syndrome is mainly manifested with imaging characteristics of unilateral seminal vesicle cyst,ipsilateral renal agenesis and ipsilateral ejaculatory duct obstruction triad.Ultrasound,CT scan,and MRI are important diagnostic tools for Zinner syndrome.Laparoscopic seminal vesicle cystectomy can reduce the risk of recurrence.
关键词
Zinner综合征/精囊囊肿/肾缺如/残余输尿管/泌尿系统Key words
Zinner syndrome/Seminal vesicle cyst/Renal agenesis/Residual ureter/Urinary system引用本文复制引用
基金项目
云南省省校合作地方高校联合专项(202001BA070001-149)
云南省卫生健康委医学后备人才培养计划(H-2018010)
出版年
2024
国家科技期刊平台
NSTL
万方数据