Hemophagocytic syndrome complicated with chronic aplastic anemia: a case report and literature review
Objective To improve the understanding of hemophagocytic syndrome. Methods Report a case of he-mophagocytic syndrome in aplastic anemia and review related literature. Results A 54-year-old female was diagnosed as chronic aplastic anemia more than 20 years ago. In this course of hospitalization, she suffered continuing hyperpyrexia and non of conclusive of infection at the beginning with serum ferritin>2 000 ng/ml, LDH 2 250 U/ L, Hypoproteinemia, serious pancytopenia and the proliferationbone of marrow cell was few awfully, lymphocyte 74% , reticular cell 26% and 6% with phagocytosis. Besides she suffered serious infection and after strengthening the treatment of anti-infection, IVIG, and so on, the clinical symptom was improved. Conclusions The clinical manifestation of hemophagocytic syndrome is hazardous, case fatality rate is high. It is very rare complicated with A A. Its function of hematopoiesis was slack up further. It is difficult to cure. Early diagnosis and treatment are critical to rescue.
NETL
NSTL
万方数据
维普
