Intrathyroid thymic carcinoma is a malignant neoplasm of thymic epithelial origin occurring in the thyroid gland. thymic carcinoma is characterized by a progressive enlargement of the neck mass and is often confused with Thyroid neoplasm. Imaging was the most commonly used method, immunohistochemistry showed high expression of CD5 and CD117, gene detection without BRAF gene mutation, a small number of TERT promoter mutation. The final diagnosis depends on postoperative pathology and immunohistochemistry, and the treatment is mainly surgical resection. postoperative adjuvant therapy can effectively delay disease progression and recurernce rate. This review analyzed the clinical manifestations, imaging examination, histopathology, immunophenotypic features, and current treatment modalities of intrathyroid thymic carcinoma, aiming to improve clinicians' understanding of intrathyroid thymic carcinoma.