Extranodal NK/T cell lymphoma(ENKTL)is an aggressive non-Hodgkin's lymphoma that destroys the midline facial region.This article reports a rare case with a palatal ulcer as the first symptom,an initial diagno-sis of necrotizing granuloma,and a final diagnosis of ENKTL.The clinical and pathological features of this tumor were discussed and the causes of misdiagnosis were analyzed in order to provide a reference for the diagnosis and dif-ferentiation of ENKTL occurring in the palate.