Objective To analyze the causes of misdiagnosis and preventive measures of spinal dural arteriovenous fistula(SDAVF).Methods The clinical data of 3 patients with misdiagnosed SDAVF admitted from January 2020 to Decem-ber 2023 were retrospectively analyzed.Results Three patients presented with unilateral upper limb sensory disturbance,unilateral lower limb numbness and weakness,and progressive aggravation of lower limb numbness and weakness with lumbar pain.One patient was misdiagnosed as transient ischemic attack,which was not improved after treatment,and was confirmed by cervical magnetic resonance angiography.The symptoms of 1 patient misdiagnosed as myelitis worsened after glucocorticoid treat-ment,and the diagnosis was confirmed by surgical exploration.One patient misdiagnosed as lumbar disc herniation was diag-nosed by spinal digital subtraction angiography.The misdiagnosis lasted 6 d to 3 months.After diagnosis,2 patients had im-proved condition after surgical treatment,and 1 patient declined surgical treatment and was lost to follow-up.Conclusion The rare onset of SDAVF,negative magnetic resonance results,abnormal results of cerebrospinal fluid examination,false negative digital subtraction angiography of spinal cord and the superposition of various disease symptoms are all important factors leading to misdiagnosis.Clinical vigilance should be raised for suspected patients,detailed medical history should be inquired,and relevant examinations should be performed to avoid misdiagnosis.