PRIMARY LIVER LYMPHANGIOLEIOMYOMATOSIS: A REPORT OF TWO CASES AND LITERATURE REVIEW
Objective To investigate the clinical features,imaging findings,diagnosis,and treatment of primary liver lymphangioleiomyomatosis.Methods Two cases of primary liver lymphangioleiomyomatosis were reported and discussed with reference to relevant literature.Results These two patients did not have specific clinical symptoms.CT scan showed quasi-circular homogeneous low density mass with clear boundaries.MR scan showed lesions with long T1 and long T2 and high signal on diffusion-weighted imaging.Contrast enhanced CT scan showed marked inhomogeneous enhancement in arterial phase,surrounding enhanced vascular imaging,reduced enhancement in portal venous phase and equilibrium phase (still higher than the density and signal of liver parenchyma),and a tendency to homogeneous enhancement.Both patients underwent surgical treatment and a confirmed diagnosis was made by pathological examination.Conclusion Primary liver lymphangioleiomyomatosis is very rare and has no specific clinical symptoms,and a confirmed diagnosis often relies on pathological examination.High-resolution chest CT should be performed regularly after surgery for the early diagnosis of possible pulmonary involvement.
NETL
NSTL
万方数据
维普
