Objective To investigate the clinical features of hemorrhagic moyamoya disease and select exact diagnosis and treatment means in emergency. Methods The clinical features, cerebrovascular angiography results, the choice of treatment and outcome in 52 cases of hemorrhagic moyamoya disease were analyzed retrospectively. Results Patients with moyamoya disease have high risk of cerebral haemorrhage in young adults, the average age was 37. 51 ± 11. 48. The main initial symptoms were headache (28,53.8%) and disturbance of consciousnes(20,38. 5% ) respectively. According to the outcome of CT scanning, periventricular hemorrhage accounted for the most. Cerebrovascular angiography ( digital subtration angiography,DSA; multislice CT angiography,CTA) found bilateral or unilateral carotid artery stenosis as well as the moyamoya vessels at the base of the brain. Thirty-two patients received conservative management, 6 patients of these underwent neurosurgical revascularization procedures, 18 patients received surgical hematoma drainage, 2 patients refusing treatment after diagnosis. Conclusion Attention should be paid to young patients with intracerebral hemorrhage. Cerebrovascular imaging is the primary means for diagnosis of hemorrhagic moyamoya disease. Exact conservative or surgical means is important in the emergency treatment.
intracerebral hemorrhagemoyamoya diseasecerebrovascular angiographytherapy means