Peripheral primitive neuroectodermal tumor arising from the seminal vesicle:a report of one case and literature review
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维普
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目的 分析临床收治及文献报道的精囊原始神经外胚层肿瘤(PNET)患者资料,总结其临床诊疗特点,提高临床医生对该疾病的认识和诊治水平.方法 分析西安交通大学第一附属医院泌尿外科收治的1例精囊PNET患者的临床及病理资料,通过PubMed、Web of Science、中国知网等检索精囊PNET相关文献,对该罕见疾病的临床特征、病理结果和治疗方法进行总结归纳.结果 最终收集到包括本例患者在内的6例精囊PNET患者.本例患者行经腹根治性膀胱全切+前列腺/双侧精囊切除+盆腔肿瘤切除+回肠膀胱术,术后病理确诊PNET,随访32个月未出现局部复发及远处转移.结论 精囊PNET是一种恶性程度高、进展快、预后差的罕见恶性肿瘤,目前确诊主要依靠病理活检、免疫组化,手术是有效的治疗方式.
Objective To explore the clinical diagnostic and therapeutic characteristics of peripheral primitive neuroectodermal tumor(PNET).Methods A retrospective analysis was conducted on the clinicopathological data of a patient diagnosed with seminal vesicle PNET treated in our hospital.Relevant literature was retrieved in PubMed,Web of Science,and CNKI.The clinical features,pathological results,and treatment methods were reviewed.Results Including this case,a total of 6 cases were collected.This case underwent a radical cystectomy with transabdominal approach,bilateral seminal vesicle resection,pelvic tumor resection,and ileal bladder surgery.Postoperative pathology confirmed PNET.During the follow-up of 32 months,no local recurrence or distant metastasis recurred.Conclusion Seminal vesicle PNET is a rare tumor with high malignancy,rapid progression,and poor prognosis.The current diagnosis mainly relies on pathological biopsy and immunohistochemistry.Surgery is an effective treatment method.
维普
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