Paget's disease of vulva with adenocarcinoma:a case report and literature review
Paget's disease of vulva(VPD),also known as vulvar Paget's disease,is a very rare gyneco-logical malignant tumor,as its incidence is low and the clinical symptoms are not typical,therefore,the treat-ment lacks evidence-based medicine.This paper reports a case of VPD,which presents with vulva swelling,ac-companied by pruritus and pain symptoms,and is diagnosed by pathological biopsy.After admission,the team of Multidisciplinary Comprehensive Treatment of Gynecological Tumors(MDT)performed extensive vulvar excision+bilateral inguinal lymph node dissection+perianal lesion excision+pedicled skin flap transplanta-tion,and the postoperative recovery was good.This paper aims to retrospectively analyze the diagnostic and treatment process of this case and combine relevant literature to discuss the clinical diagnosis and treatment of VPD,in order to provide reference for the diagnosis and treatment of VPD.
Paget's disease of vulvaAdenocarcinomaDiagnosisCase report