The clinical value of echocardiography in the preoperative diagnosis and postoperative evaluation of children with Shone's syndrome and the analysis of misdiagnosis
The clinical value of echocardiography in the preoperative diagnosis and postoperative evaluation of children with Shone's syndrome and the analysis of misdiagnosis
Objective:To investigate the clinical value of echocardiography in the preoperative diagnosis,postoperative follow-up and evaluation of surgical effect of Shone's syndrome,and to summarize the reasons of misdiagnosis to improve the understanding and diagnosis rate of this malformation.Methods:From January 2014 to January 2023,the echocardiography and clinical data of 63 patients with Shone's syndrome and confirmed by surgery were retrospectively analyzed,and the abnormalities diagnosed by ultrasound and observed during surgery were compared.Echocardiography was performed before and 1 month and 1 year after surgery,and the peak pressure difference between mitral valve,left ventricular outflow tract and descending aortic arch was measured and statistically compared.Results:The missed diagnosis rate of left ventricular outflow tract malformation by echocardiography was lower than that of left ventricular inflow tract malformation,and the missed rate of intra-valvular ring was the highest,There was no missed diagnosis of coarctation,dysplasia,and aortic stenosis,and the missed diagnosis rate of residual malformations was less than 20%.The postoperative pressure was significantly lower than that before operation,and the differences were statistically significant(all P<0.01).There was no significant difference at 1 month and 1 year after surgery(P>0.05).Conclusion:Echocardiography can provide early and accurate diagnosis of Shone's syndrome,and provide a reliable basis for further surgical treatment and postoperative follow-up,which has important clinical value.