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先天性巨结肠相关性小肠结肠炎诊断评分的研究进展

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先天性巨结肠相关性小肠结肠炎(Hirschsprung associated enterocolitis,HAEC)是先天性巨结肠的一种特别严重的并发症,其特征是爆发性腹泻(通常为血性)、发热和腹胀,严重威胁患儿生命安全.目前对HAEC诊断评分标准并未达成共识,亟需构建更合理的评分系统辅助尽早诊断及干预.本研究对先天性巨结肠相关性小肠结肠炎诊断评分的研究进展进行综述,以期为HAEC的早期诊断以及改善患儿预后提供参考.
Research advances on the diagnostic score of Hirschsprung-associated enterocolitis
As a particularly severe complication of Hirschsprung's disease(HD),Hirschsprung associated enterocolitis(HAEC)is characterized by explosive diarrhea(usually bloody),fever and abdominal distension.Currently there is no consensus on diagnostic score of HAEC.Thus it is imperative to construct a more reasonable scoring system for early diagnosis and intervention.Summarizing the latest researches of diagnostic scores for HAEC,this review provides references for an early diagnosis of HAEC and improving the outcomes.

Hirschsprung diseaseEnterocolitisDiagnosis

赵志威、华子瑜

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重庆医科大学附属儿童医院,重庆 400014

先天性巨结肠 小肠结肠炎 诊断

2024

中华小儿外科杂志
中华医学会

中华小儿外科杂志

CSTPCD北大核心
影响因子:0.853
ISSN:0253-3006
年,卷(期):2024.45(5)