Fibrosing mediastinitis(FM)is also known as sclerosing mediastinitis or mediastinal fibrosis,it is a rare disease characterized by benign hyperplasia of mediastinal fibrous tissue.With the proliferation of fibrous tissue in the mediastinum,corresponding compression symptoms gradually appear after compression of blood vessels,trachea and esophagus.In the early stage of disease progression,there may be no clinical manifestations obviously,and it is easy to misdiagnose.Due to the rarity of FM and the small sample size of cases,the clinical research is limited,the etiology and pathogenesis are still unclear,and there is no standardized diagnosis and treatment guideline of FM.This article expounds the research status of pulmonary artery stenosis caused by FM,aiming to provide guidance for the diagnosis and treatment of pulmonary artery stenosis associated with FM.
关键词
纤维性纵隔炎/纤维组织增生/肺动脉狭窄/诊疗
Key words
Fibrosing mediastinitis/Proliferation of fibrous tissue/Pulmonary artery stenosis/Diagnosis and treatment
维普
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