New Era of Fontan Circulation—Research Progress in Long-Term Lymphatic System Complications
Total cavopulmonary connection(Fontan procedure)has saved the lives of a large number of children with single ventricle,in which a biventricular repair is not possible.However,postoperative long-term lymphatic system complications seriously affect the prognosis of patients.This article reviews the previous literature and summarizes the natural history,pathophysiology,clinical manifestations,diagnosis,and management of lymphatic system complications in patients with Fontan circulation.
Fontan circulationLymphatic system complicationsPlastic bronchitisProtein-losing enteropathyLymphatic interventional therapy