Objective To analyze the imaging features of clear cell sarcoma of kidney(CCSK)in children,summarize the imaging and clinical features of CCSK,explore the factors of misdiagnosis,improve the recognition of CCSK,and improve the diagnostic coincidence rate.Methods The imaging data of 11 patients with CCSK diagnosed by pathology in Henan Children's Hospital were retrospectively analyzed.All the children underwent CT scan.The imaging and clinical manifestations were summarized,and the factors of misdiagnosis were analyzed.Results The tumors were unilateral in all cases,including 5 cases in the right kidney and 6 cases in the left kidney.The age range of the 11 cases was from May 9 to 10 years old.The tumors were mostly large and mixed in density,all of them were single,and 10 cases had cystic change.Multiple small arteries were found in 9 cases,and the solid components showed delayed and progressive enhancement.2 cases were accompanied by inferior vena cava and ipsilateral renal vein cancer embolus.There were 7 cases of perirenal vascular filling,2 cases of bone metastasis and calcification,and 1 case of subcapsular effusion.10 patients were misdiagnosed with nephroblastoma(WT)before operation,of which 8 were misdiagnosed with WT,1 was misdiagnosed with congenital mesoblastoma,and 1 was misdiagnosed with renal rhabdomyoma.Conclusion In terms of imaging manifestations,CCSK is highly similar to other pediatric renal tumors,especially nephroblastoma,with high probability of preoperative misdiagnosis,young age of onset,poor prognosis,rapid progression of the disease,prone to cystic change and necrosis,enhancement of multiple small arteries in the tumor,delayed progressive enhancement,and fish,tiger,stripe or cloudy enhancement.Perirenal vascular filling is common and helps to distinguish it from other renal tumors.
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万方数据