Epithelioid hemangioendothelioma(EHE)is a rare vascular tumor with histological features between hemangiomas and high-grade angiosarcomas.Because its imaging and histological features are similar to hemangiomas or metastatic spinal tumors,accurate diagno-sis and effective treatment of spinal EHE are particularly important.From some of the reported spinal EHE,we can note that there are cer-tain similarities in its diagnosis and treatment,and this article reports one case of spinal EHE,and reviews and summarizes the published lit-erature on spinal EHE.