Objective To explore the ICD-10 coding of pheochromocytoma and paraganglioma.Methods By introdu-cing the different pathological characteristics of tumors and three clinical cases,a retrospective analysis was conducted on cases of incorrect coding.The coding ideas and methods of tumors were sorted out,and the reasons for coding errors were summarized.Results The classification of pheochromocytoma/paraganglioma is complex and the morphology is variable.It is easily confused with other tumors or the benign and malignant tumors can not be distinguished,resulting in coding errors.Conclusion Coders should strictly follow the coding rules and steps of the International Classification of Diseases,carefully read medical records,and actively communicate with clinical and pathological doctors to ensure coding quality and improve the accuracy of their disease cod-ing.