Nephrogenic adenoma of the ureter is very rare clinically.One case with nephrogenic adenoma of the ureter was reported,which was suspected of bladder cancer by CT examination.Cystoscopy was successfully performed,and pathological diagnosis was nephrogenic adenoma.Bilateral partial ureterectomy and ureteroneocystomy were performed.Recurrence or metastasis was not demonstrated by the follow-up of 26 months.