Epidermolysis bullosa is a rare group of hereditary diseases.Besides skin tissue,the lesions can also involve the urinary system.However,due to its low incidence rate and lack of clinical recognition,it is easy to be ignored in the early stage of onset.When it is paid attention to,it often has developed to the degree of renal dysfunction or urethral stricture,and the opportunity for early intervention is lost.This not only brings difficulties to treatment,but also increases physical and mental pain to patients.This article reviewed the pathogenesis,classification,diagnosis and treatment of epidermolysis bullosa involving the urinary system,in order to provide reference for future clinical diagnosis and treatment.
维普
万方数据
