新发难治性癫痫持续状态/热性感染相关性癫痫综合征:癫痫持续状态诊疗的新挑战
New onset refractory status epilepticus/febrile infection-related epilepsy syndrome:the new challenge in the diagnosis and treatment of status epilepticus
王萱 1江文1
作者信息
- 1. 空军军医大学西京医院神经内科,西安 710032
- 折叠
摘要
新发难治性癫痫持续状态(NORSE)及其亚类热性感染相关性癫痫综合征(FIRES)常以难治性癫痫持续状态起病,具有高病死率、高致残性的特点.由于发病机制不清,诊疗极具挑战.文中将从NORSE/FIRES定义、病因与致病机制、临床特点、治疗与预后等多个方面进行评述.
Abstract
New onset refractory status epilepticus(NORSE)and its subcategory,febrile infection-related epilepsy syndrome(FIRES)are rare and devastating conditions,initial symptoms of which are often refractory status epilepticus.NORSE/FIRES is characterized by high mortality and disability,but unfortunately,due to the unclear pathogenesis,the diagnosis and treatment of NORSE/FIRES are very challenging.This editorial aims to summarize the key points and recent developments in the etiology,pathophysiology,diagnosis and management of these challenging conditions.
关键词
新发难治性癫痫持续状态/热性感染相关性癫痫综合征/药物难治性癫痫/免疫治疗Key words
New onset refractory status epilepticus/Febrile infection-related epilepsy syndrome/Drug resistant epilepsy/Immunological treatment引用本文复制引用
出版年
2024
NETL
NSTL
万方数据