自身免疫性郎飞结病诊断和治疗中国专家共识2023
Chinese expert consensus on the diagnosis and treatment of autoimmune nodopathy 2023
中华医学会神经病学分会 中华医学会神经病学分会周围神经病协作组 刘明生 1蒲传强 2崔丽英1
作者信息
- 1. 中国医学科学院北京协和医院神经科,北京100730
- 2. 解放军总医院神经内科,北京100853
- 折叠
摘要
自身免疫性郎飞结病是一类由免疫介导的周围神经病,血清中可检测到抗郎飞结抗体.随着研究的不断深入,近年来针对自身免疫性郎飞结病的认识已经比较清晰,目前普遍认为应该将其从慢性炎性脱髓鞘性多发性神经根神经病中独立出来.为提高我国神经科医生对该病的认识,规范临床诊治,中华医学会神经病学分会周围神经病协作组组织该领域国内专家进行讨论,结合国内外研究进展以及国内专家的经验,制订了自身免疫性郎飞结病诊断和治疗中国专家共识,其内容包括自身免疫性郎飞结病的临床、神经电生理、脑脊液、周围神经影像学、腓肠神经病理特点,抗体检测以及该疾病的诊断标准和治疗要点.
Abstract
Autoimmune nodopathy is a group of immune-mediated peripheral neuropathy,and antibodies to Ranvier nodal regions can be detected in serum.With the deepening of research,the understanding of autoimmune nodopathy has been relatively clear in recent years,and it is generally believed that it should be separated from chronic inflammatory demyelinating polyradiculoneuropathy.In order to improve the understanding of neurologists in China and standardize the clinical diagnosis and treatment of the disease,the Peripheral Neuropathy Collaboration Group of Chinese Society of Neurology organized repeated discussions among domestic experts in this field,combined with the research progress at home and abroad and the experience of domestic experts,formulated a consensus on the diagnosis and treatment of autoimmune nodopathy,which includes the clinical features,neuroelectrophysiology,cerebrospinal fluid,peripheral nerve imaging,sural neuropathological characteristics,antibody detection,diagnostic criteria and treatment points of autoimmune nodopathy.
关键词
周围神经病/郎飞结/诊断/治疗/共识Key words
Peripheral neuropathy/Ranvier's nodes/Diagnosis/Treatment/Consensus引用本文复制引用
出版年
2024
NETL
NSTL
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