Ocular adnexal lymphoma is a common malignant tumor of adult ocular adnexa, which has complex pathological types and various clinical features and can occur at any age.The positron emission tomography-computed tomography(PET-CT) can provide the evidence for the formulation of initial staging and treatment strategy, which is also used to evaluate the efficacy and prognosis of ocular adnexal lymphoma. The progress of PET-CT in the clinical application of ocular adnexal lymphoma was reviewed in this paper.